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KMID : 0366219890240020543
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Korean Journal of Hematology
1989 Volume.24 No. 2 p.543 ~ p.549
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A Case Showing Glucose-induced more Increased Autohemolysis in Hemolytic Crisis of Hereditary Spherocytosis
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김동준/Dong Jun Kim
김태빈/최문기/박찬정/박영의/이영주/Tae Bin Kim/Moon Ki Choi/Chan Jung Park/Young Eui Park/Young Joo Lee
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Abstract
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Hereditary spherocytosis is one of the common inherited disorders of the red cell
membrane, characterized by osmotically fragile spherical red cells that are selectively
trapped by the spleen. Increased autohemolysis with the partial protecting effects of
added glucose is a common finding in hereditary spherocytosis. But in some rare cases,
glucose fails to prevent the increased autohemolysis. We experienced a case of
hereditary spherocytosis in 21-year old female patient whose clinical and laboratory
features showed typical findings of hereditary spherocytosis except autohemolysis test in
which added glucose did not prevent increased autohemolysis, After splenectomy the
symptoms and signs disappeared, the laboratory data improved and the autohemolysis
test showed typical findings of hereditary spherocytosis.
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KEYWORD
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